3-Hydroxypropionate

ChemistryAlso known as: 3oh-propionic acidAlso known as: β-Hydroxypropionic acidAlso known as: β-HydroxypropionateN/A

Detects 3-hydroxypropionate in urine, indicating organic acid metabolism dysfunction.

Normal Range

Consult your provider

N/A

Abnormal Levels

Consult your provider

Specimen Type

Blood

Why This Biomarker Matters

Presence suggests rare genetic organic acid disorders. Early detection enables specialized nutritional management and prevents serious metabolic complications.

Overview

3-Hydroxypropionate is an organic acid excreted in urine that reflects abnormal metabolism of certain amino acids and fatty acids. Its presence suggests possible propionyl-CoA carboxylase deficiency (propionic acidemia) or other organic acid disorders affecting amino acid and fatty acid breakdown. These are rare genetic metabolic conditions that can cause neurological problems, developmental delays, and metabolic crises. Detection of 3-hydroxypropionate helps identify these serious conditions early for specialized dietary and medical management.

Research & Evidence

1 publications

Metabolic engineering enablesto grow on 1,3-propanediol.

Synth Syst Biotechnol · 2026

PMID: 41536924Other

Research data from MEDLINE/PubMed · 1 articles

Technical Information (LOINC Codes)

Standardized laboratory codes for this biomarker

29625-1Primary

3-Hydroxypropionate (3-OH-C3) [Presence] in Urine

47536-8

3-Hydroxypropionate (3-OH-C3) [Moles/volume] in Plasma

umol/L

50128-8

3-Hydroxypropionate (3-OH-C3) [Moles/volume] in Cerebral spinal fluid

umol/L

50129-6

3-Hydroxypropionate (3-OH-C3) [Moles/volume] in Amniotic fluid

umol/L

Available Lab Tests

Order tests that measure this biomarker

Urinary Organic Acids (94 biomarkers)

$586.08

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