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Ataxia-telangiectasia-like disorder

disorder
SNOMED 700058006CUI C1858391

Overview

Ataxia-telangiectasia-like disorder is a disorder.

Auto-generated from clinical reference data. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Unsteady walk
Always present (100%)HP:0002317
Ataxia
Very frequent (80-99%)HP:0001251
Abnormal finger-nose-finger test
Frequent (30-79%)HP:0001310
Absent Achilles reflex
Frequent (30-79%)HP:0003438
Cerebellar tremor
Frequent (30-79%)HP:0002080
Cerebellar vermis hypoplasia
Frequent (30-79%)HP:0001320
Choreoathetoid movements
Frequent (30-79%)HP:0001266
Defective or absent horizontal voluntary eye movements
Frequent (30-79%)HP:0000657
Difficulty articulating speech
Frequent (30-79%)HP:0001260
Dilated fourth ventricle
Frequent (30-79%)HP:0002198
Diminished deep tendon reflexes
Frequent (30-79%)HP:0001315
Dystonic disease
Frequent (30-79%)HP:0001332
Enlarged longitudinal cerebral fissure
Frequent (30-79%)HP:0100953
Generalised decreased muscle tone
Frequent (30-79%)HP:0001290
Horizontal jerk nystagmus
Frequent (30-79%)HP:0007286
Inability to coordinate movements when walking
Frequent (30-79%)HP:0002066
Mask-like facies
Frequent (30-79%)HP:0000298
Orofacial dyskinesias
Frequent (30-79%)HP:0002310
Peripheral hypotonia
Frequent (30-79%)HP:0001252
Slow visual tracking
Frequent (30-79%)HP:0000514
Cavus foot
Occasional (5-29%)HP:0001761
Dysdiadochokinesis
Occasional (5-29%)HP:0002075
Dysmetric eye movements
Occasional (5-29%)HP:0000641
Gaze-evoked nystagmus
Occasional (5-29%)HP:0000640
Hyperactive deep tendon reflexes
Occasional (5-29%)HP:0006801
Impaired smooth pursuit ocular movements
Occasional (5-29%)HP:0000617
Jerking
Occasional (5-29%)HP:0001336
Joint instability
Occasional (5-29%)HP:0001382
Nerve damage causing decreased feeling and movement
Occasional (5-29%)HP:0007141
Primary hypogonadism
Occasional (5-29%)HP:0000815

Quick Facts

SNOMED CT
700058006
UMLS CUI
C1858391
Fully Specified Name
Ataxia-telangiectasia-like disorder (disorder)
Specialists
0
Diagnostic Biomarkers
0
HPO Phenotypes
30
Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.