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Bietti's crystalline retinopathy

disorder
SNOMED 312927001CUI C1859486

Overview

Source: MedlinePlus.gov, National Library of Medicine. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Decreased visual acuity
Very frequent (80-99%)HP:0007663
Choriocapillaris atrophy
Frequent (30-79%)HP:0030491
Constriction of peripheral visual field
Frequent (30-79%)HP:0001133
Corneal deposits
Frequent (30-79%)HP:0000531
Crystalline corneal dystrophy
Frequent (30-79%)HP:0007760
Decreased light- and dark-adapted electroretinogram amplitude
Frequent (30-79%)HP:0000654
Difficulties with night vision
Frequent (30-79%)HP:0000662
Impaired vision
Frequent (30-79%)HP:0000505
Retinal pigment epithelial atrophy
Frequent (30-79%)HP:0007722
Subretinal deposits
Frequent (30-79%)HP:0031528
Blind spot located at fixation point
Occasional (5-29%)HP:0000603
Blindness
Occasional (5-29%)HP:0000618
Cystoid macular edema
Occasional (5-29%)HP:0011505
Large central loss of field of vision
Occasional (5-29%)HP:0001129
Loss in color vision
Occasional (5-29%)HP:0000551
Paracentral scotoma
Occasional (5-29%)HP:0030528
Retinal pigmentary degeneration
Occasional (5-29%)HP:0000580
Retinal thinning
Occasional (5-29%)HP:0030329
RPE irregularity
Occasional (5-29%)HP:0007814
Severe myopia
Occasional (5-29%)HP:0011003
Severely impaired vision
Occasional (5-29%)HP:0001141
Chorioretinal atrophy
HP:0000533
Decreased visual acuity, progressive
HP:0000529
Marginal corneal dystrophy
HP:0007880
Progressive night blindness
HP:0007675
Retinal degeneration
HP:0000546

Quick Facts

SNOMED CT
312927001
UMLS CUI
C1859486
Fully Specified Name
Bietti's crystalline retinopathy (disorder)
Specialists
0
Diagnostic Biomarkers
0
HPO Phenotypes
26
Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.