PAIV - Pulmonary atresia with intact ventricular septum

disorder

SNOMED 253590009CUI C0344975

Overview

Source: MedlinePlus.gov, National Library of Medicine. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Abnormal tricuspid valve morphology

Very frequent (80-99%)HP:0001702

Atresia of the pulmonary artery

Very frequent (80-99%)HP:0004935

PDA

Frequent (30-79%)HP:0001643

Premature birth

Frequent (30-79%)HP:0001622

Hypoplastic right heart syndrome

HP:0010954

Related Conditions

Atresia of pulmonary valve(parent)

Quick Facts

SNOMED CT: 253590009
UMLS CUI: C0344975
Fully Specified Name: Pulmonary atresia with intact ventricular septum (disorder)
Specialists: 0
Diagnostic Biomarkers: 0
HPO Phenotypes: 5

Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.