Primary pauci-immune necrotising and crescentic glomerulonephritis

disorder

SNOMED 239932005CUI C0343196

Overview

Primary pauci-immune necrotising and crescentic glomerulonephritis is a disorder.

Auto-generated from clinical reference data. Not a substitute for medical advice.

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Glomerulonephritis

Always present (100%)HP:0000099

Anti-neutrophil cytoplasmic antibody positivity

Very frequent (80-99%)HP:0032230

Decreased glomerular filtration rate

Very frequent (80-99%)HP:0012213

Increased creatinine

Very frequent (80-99%)HP:0003259

Microhematuria

Very frequent (80-99%)HP:0002907

Proteinuria

Very frequent (80-99%)HP:0000093

Renal failure

Very frequent (80-99%)HP:0000083

Small vessel vasculitis

Very frequent (80-99%)HP:0011944

Abnormality of the respiratory system

Frequent (30-79%)HP:0002086

Crescentic glomerulonephritis

Frequent (30-79%)HP:0008653

Dermatopathy

Frequent (30-79%)HP:0000951

Glomerulosclerosis

Frequent (30-79%)HP:0000096

Pyrexia

Frequent (30-79%)HP:0001945

Abnormal eye

Occasional (5-29%)HP:0000478

Abnormality of the pulmonary vasculature

Occasional (5-29%)HP:0004930

Abnormality of the upper respiratory tract

Occasional (5-29%)HP:0002087

Acute kidney failure

Occasional (5-29%)HP:0001919

Antinuclear antibodies

Occasional (5-29%)HP:0003493

Arthritic pain

Occasional (5-29%)HP:0002829

Blood spots

Occasional (5-29%)HP:0000979

Coughing

Occasional (5-29%)HP:0012735

Difficulty breathing

Occasional (5-29%)HP:0002094

Husky voice

Occasional (5-29%)HP:0001609

Inflammation of artery

Occasional (5-29%)HP:0012089

Intrapulmonary hemorrhage

Occasional (5-29%)HP:0040223

Macroscopic hematuria

Occasional (5-29%)HP:0012587

Nephrotic range proteinuria

Occasional (5-29%)HP:0012593

Tubulointerstitial nephritis

Occasional (5-29%)HP:0001970

Upset stomach

Occasional (5-29%)HP:0002027

Cardiovascular disease

Very rare (1-4%)HP:0001626

Related Conditions

Glomerulonephritis(parent)

Rapidly progressive glomerulonephritis(parent)

Necrosis of cortex of kidney(parent)

Quick Facts

SNOMED CT: 239932005
UMLS CUI: C0343196
Fully Specified Name: Primary pauci-immune necrotizing and crescentic glomerulonephritis (disorder)
Specialists: 0
Diagnostic Biomarkers: 0
HPO Phenotypes: 30

Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.